Long-chain specific acyl-CoA dehydrogenase, mitochondrial belongs to the acyl-CoAdehydrogenase family, which is a family of mitochondrialflavoenzymes involved in fatty acid and branched chain amino-acidmetabolism. This protein is one of the four enzymes that catalyzethe initial step of mitochondrial beta-oxidation of straight-chainfatty acid. Defects in this gene are the cause of long-chainacyl-CoA dehydrogenase (LCAD) deficiency, leading to nonketotichypoglycemia.
Titration of the ACADL antibody may be required due to differences in protocols and secondary/substrate sensitivity.
A portion of amino acids 14-43 from the human protein was used as the immunogen for this ACADL antibody.
Aliquot the ACADL antibody and store frozen at -20oC or colder.Avoid repeated freeze-thaw cycles.
